Outcome of elexacaftor/tezacaftor/ivacaftor therapy in patients with cystic fibrosis and solid organ transplantation

Matilde B. Ørum; Frederikke F. Rönsholt; Majbritt Jeppesen; Elisabeth Bendstrup; Terese L. Katzenstein; Peter Ott; Michael Perch; Tacjana Pressler; Tavs Qvist; Søren Jensen-Fangel

doi:10.1002/ppul.26217

Outcome of elexacaftor/tezacaftor/ivacaftor therapy in patients with cystic fibrosis and solid organ transplantation

Matilde B. Ørum^*, Frederikke F. Rönsholt, Majbritt Jeppesen, Elisabeth Bendstrup, Terese L. Katzenstein, Peter Ott, Michael Perch, Tacjana Pressler, Tavs Qvist, Søren Jensen-Fangel

^*Corresponding author for this work

Research output: Contribution to journal/Conference contribution in journal/Contribution to newspaper › Journal article › Research › peer-review

7 Citations (Scopus)

Abstract

We report a case series of four patients with cystic fibrosis (CF) and previous solid organ transplantation (SOT) receiving elexacaftor/tezacaftor/ivacaftor therapy for 6 months or more. Data was collected retrospectively. The treatment was well tolerated and all patients reported subjective improvements.

Original language	English
Journal	Pediatric Pulmonology
Volume	58
Issue	2
Pages (from-to)	602-605
Number of pages	4
ISSN	8755-6863
DOIs	https://doi.org/10.1002/ppul.26217
Publication status	Published - Feb 2023

Keywords

CFTR therapy
cystic fibrosis
cystic fibrosis transmembrane conductance regulator therapy
ETI
solid organ transplantation

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10.1002/ppul.26217

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title = "Outcome of elexacaftor/tezacaftor/ivacaftor therapy in patients with cystic fibrosis and solid organ transplantation",

abstract = "We report a case series of four patients with cystic fibrosis (CF) and previous solid organ transplantation (SOT) receiving elexacaftor/tezacaftor/ivacaftor therapy for 6 months or more. Data was collected retrospectively. The treatment was well tolerated and all patients reported subjective improvements.",

keywords = "CFTR therapy, cystic fibrosis, cystic fibrosis transmembrane conductance regulator therapy, ETI, solid organ transplantation",

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Outcome of elexacaftor/tezacaftor/ivacaftor therapy in patients with cystic fibrosis and solid organ transplantation. / Ørum, Matilde B.; Rönsholt, Frederikke F.; Jeppesen, Majbritt et al.
In: Pediatric Pulmonology, Vol. 58, No. 2, 02.2023, p. 602-605.

Research output: Contribution to journal/Conference contribution in journal/Contribution to newspaper › Journal article › Research › peer-review

TY - JOUR

T1 - Outcome of elexacaftor/tezacaftor/ivacaftor therapy in patients with cystic fibrosis and solid organ transplantation

AU - Ørum, Matilde B.

AU - Rönsholt, Frederikke F.

AU - Jeppesen, Majbritt

AU - Bendstrup, Elisabeth

AU - Katzenstein, Terese L.

AU - Ott, Peter

AU - Perch, Michael

AU - Pressler, Tacjana

AU - Qvist, Tavs

AU - Jensen-Fangel, Søren

PY - 2023/2

Y1 - 2023/2

N2 - We report a case series of four patients with cystic fibrosis (CF) and previous solid organ transplantation (SOT) receiving elexacaftor/tezacaftor/ivacaftor therapy for 6 months or more. Data was collected retrospectively. The treatment was well tolerated and all patients reported subjective improvements.

AB - We report a case series of four patients with cystic fibrosis (CF) and previous solid organ transplantation (SOT) receiving elexacaftor/tezacaftor/ivacaftor therapy for 6 months or more. Data was collected retrospectively. The treatment was well tolerated and all patients reported subjective improvements.

KW - CFTR therapy

KW - cystic fibrosis

KW - cystic fibrosis transmembrane conductance regulator therapy

KW - ETI

KW - solid organ transplantation

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DO - 10.1002/ppul.26217

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JO - Pediatric Pulmonology

JF - Pediatric Pulmonology

IS - 2

ER -

Outcome of elexacaftor/tezacaftor/ivacaftor therapy in patients with cystic fibrosis and solid organ transplantation

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