Elisabeth Bendstrup

Idiopathic Pulmonary Fibrosis: Best Practice in Monitoring and Managing a Relentless Fibrotic Disease

Research output: Contribution to journal/Conference contribution in journal/Contribution to newspaperReviewResearchpeer-review

DOI

  • Wim A. Wuyts, KU Leuven
  • ,
  • Marlies Wijsenbeek, Erasmus University Rotterdam
  • ,
  • Benjamin Bondue, Université Libre de Bruxelles
  • ,
  • Demosthenes Bouros, University of Athens
  • ,
  • Paul Bresser, Onze Lieve Vrouwe Gasthuis
  • ,
  • Carlos Robalo Cordeiro, University of Coimbra
  • ,
  • Ole Hilberg
  • ,
  • Jesper Magnusson, University of Gothenburg
  • ,
  • Effrosyni D. Manali, University of Athens
  • ,
  • António Morais, Sao Joao Hospital
  • ,
  • Spyridon Papiris, University of Athens
  • ,
  • Saher Shaker, University of Copenhagen
  • ,
  • Marcel Veltkamp, St. Antonius Ziekenhuis
  • ,
  • Elisabeth Bendstrup

Idiopathic pulmonary fibrosis (IPF) is a fibrosing interstitial lung disease that is, by definition, progressive. Progression of IPF is reflected by a decline in lung function, worsening of dyspnea and exercise capacity, and deterioration in health-related quality of life. In the short term, the course of disease for an individual patient is impossible to predict. A period of relative stability in forced vital capacity (FVC) does not mean that FVC will remain stable in the near future. Frequent monitoring using multiple assessments, not limited to pulmonary function tests, is important to evaluate disease progression in individual patients and ensure that patients are offered appropriate care. Optimal management of IPF requires a multidimensional approach, including both pharmacological therapy to slow decline in lung function and supportive care to preserve patients' quality of life.

Original languageEnglish
JournalRespiration
Volume99
Issue1
Pages (from-to)73-82
Number of pages10
ISSN0025-7931
DOIs
Publication statusPublished - 2020

    Research areas

  • Interstitial lung disease, Mortality, Nintedanib, Pirfenidone, Therapeutics, Treatment

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