Dorte Guldbrand Nielsen

Rupture of an Abdominal Aortic Aneurysm in a Young Man with Marfan Syndrome

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  • Maria Weinkouff Pedersen, Aalborg University
  • ,
  • Khiem Dinh Huynh, Department of Vascular Surgery, Aalborg Hospital
  • ,
  • Ulrik Thorngren Baandrup, Department of Pathology, Center for Clinical Research, Vendsyssel Hospital, Aalborg University
  • ,
  • Dorte Guldbrand Nielsen
  • Niels Holmark Andersen, Aalborg University

Abdominal aortic aneurysms (AAAs) are very rare in Marfan syndrome. We present a case with a young nonsmoking and normotensive male with Marfan syndrome, who developed an infrarenal AAA that presented with rupture to the retroperitoneal cavity causing life-threatening bleeding shock. The patient had acute aortic surgery and survived. Five months before this incident, the patient had uneventful elective aortic root replacement (ad modum David) due to an enlarged aortic root. At that time, his abdominal aorta was assessed with a routine ultrasound scan that showed a normal-sized abdominal aorta. This documents that the aneurysm had evolved very rapidly despite young age and absence of risk factors.

Original languageEnglish
JournalAnnals of Vascular Surgery
Volume48
Pages (from-to)252.e5-252.e8
Number of pages4
ISSN0890-5096
DOIs
Publication statusPublished - 1 Apr 2018

Bibliographical note

Copyright © 2018 Elsevier Inc. All rights reserved.

    Research areas

  • Aortic Aneurysm, Abdominal/diagnostic imaging, Aortic Rupture/diagnostic imaging, Aortography/methods, Biopsy, Blood Vessel Prosthesis Implantation, Computed Tomography Angiography, Humans, Male, Marfan Syndrome/complications, Treatment Outcome, Ultrasonography, Young Adult

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